AIIMS Nagpur NO- 2020
Child Health Nursing (Pediatrics)
Easy

Additional defects associated with exstrophy of bladder is:

Appeared in: AIIMS Nagpur NO- 2020

Explanation

  • Bladder exstrophy is a congenital anomaly where the bladder protrudes through a defect in the lower abdominal wall.
  • A defining characteristic of bladder exstrophy is a malformation of the pelvic bones.
  • Specifically, the pubic bones are widely separated (a condition called pubic diastasis), which is a direct consequence of the developmental failure.
  • This bony defect is clearly visible in the provided diagram and is a consistent finding in this condition.

Why Other Options Were Wrong

  • Option A: Congenital heart disease is not considered a primary or hallmark associated defect of classic bladder exstrophy.
  • Option C: In classic bladder exstrophy, the upper urinary tracts, including the kidneys, are usually normal at birth. Unilateral renal agenesis is not a typical associated finding.
  • Option D: Imperforate anus is a key feature of a different, more severe condition known as cloacal exstrophy (or OEIS complex), not classic bladder exstrophy.

Related Visual

Visual explanation — Related Visual
Clinical Relevance
  • Nursing practice connection: This is primarily an exam-oriented knowledge point with limited direct bedside application, so retain Associated anomalies in bladder exstrophy as background academic context rather than a clinical decision trigger.
  • Immediate nursing care for a newborn with bladder exstrophy involves protecting the exposed bladder mucosa from injury, infection, and drying. This is done by covering the bladder with a sterile, non-adherent plastic wrap or film.
  • The pubic bone malformation is clinically significant as it necessitates a pelvic osteotomy during surgical repair to provide a stable foundation for the bladder and abdominal wall closure.
  • Long-term, the altered pelvic anatomy can lead to a characteristic waddling gait, although most children adapt well without significant disability.
How to Approach the Question
  • First, analyze the question, which asks for a defect associated with bladder exstrophy.
  • Next, carefully examine the provided image. Identify the key anatomical abnormalities shown: an exposed bladder on the abdomen and a clear separation between the pelvic bones.
  • Evaluate each option against your visual analysis and clinical knowledge.
  • Option B, 'Pubic bone malformation,' directly corresponds to the separated pelvic bones seen in the image.
  • Consider the other options. Congenital heart disease and absence of a kidney are not classic features. 'Imperforate anus' (corrected from 'rash') is a feature of a different, more severe condition (cloacal exstrophy).
  • Conclude that the pubic bone malformation is the most consistent and defining associated defect of bladder exstrophy.
Concept Tested & Keywords
  • Concept Tested: Associated anomalies in bladder exstrophy
  • Stem keywords: exstrophy of bladder, additional defects
  • Lead-in keywords: is
  • Clinical cues: The image shows a newborn with an exposed bladder and separated pubic bones, which are classic signs of bladder exstrophy.

Question ID

QEwT8tbx26vevh6W1xoc9X

Reference Book

E6 Nelson Textbook of Pediatrics(2024) — Volume 2 p. 1088-1090

E6 Obstetrics Williams p. 24-43

E6 Gynecology Williams p. 12

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