NORCET 9 Mains - 2025
Child Health Nursing (Pediatrics)
Easy

In a newborn with spina bifida myelomeningocele, which clinical sign most strongly suggests an associated complication?

Appeared in: NORCET 9 Mains - 2025

Explanation

  • Myelomeningocele, the most severe form of spina bifida, is frequently associated with hydrocephalus (excess cerebrospinal fluid in the brain's ventricles).
  • This complication is typically caused by an accompanying Chiari II malformation, which obstructs the normal flow of cerebrospinal fluid (CSF).
  • The resulting increase in intracranial pressure (ICP) causes the fontanelles (soft spots) on an infant's skull to bulge, as the cranial sutures have not yet fused.
  • Therefore, a bulging fontanelle is a classic and urgent sign of this common and serious complication.

Why Other Options Were Wrong

  • Option B: A tuft of hair over the lumbosacral area is a characteristic sign of spina bifida occulta, the mildest form of neural tube defect where the spinal cord is not exposed. It is not a complication of myelomeningocele.
  • Option C: A sunken fontanelle is a classic sign of dehydration, indicating a deficit of body fluid. This is the opposite of the fluid accumulation (hydrocephalus) that complicates myelomeningocele.
  • Option D: Myelomeningocele involves damage to the lower spinal cord and nerve roots (lower motor neurons). This results in flaccid paralysis, muscle weakness, and absent or diminished deep tendon reflexes below the level of the lesion.

Related Visual

Visual explanation — Related Visual
  • Visual 1: Diagram: Pathophysiology of Hydrocephalus in Myelomeningocele. A visual showing the Chiari II malformation obstructing CSF flow from the fourth ventricle, leading to ventricular enlargement.
  • Visual 2: Illustration: Comparison of Infant Fontanelles. An image comparing a normal flat fontanelle, a bulging/tense fontanelle (indicating increased ICP), and a sunken fontanelle (indicating dehydration).
  • Visual 3: Photo: Prone Positioning for Myelomeningocele. A clinical photo demonstrating the correct way to position an infant with an exposed myelomeningocele sac to prevent pressure and injury.
Clinical Relevance
  • Nursing practice connection: Knowing Assessment of Complications in Myelomeningocele helps nurses interpret findings accurately and avoid errors in routine assessment, medication administration, and patient teaching.
  • Early detection of hydrocephalus is a critical nursing responsibility. Daily head circumference measurement and fontanelle assessment are mandatory for any newborn with myelomeningocele.
  • A bulging fontanelle is a neurological red flag. It requires immediate notification of the medical team, as it may signal the need for urgent neurosurgical intervention, such as the placement of a ventriculoperitoneal (VP) shunt.
  • What if? If the patient were an older child whose fontanelles had already closed, the signs of increased ICP would be different. Instead of a bulging fontanelle, the nurse would look for headache, nausea/vomiting (especially in the morning), lethargy, irritability, and vision changes (papilledema).
How to Approach the Question
  • First, identify the patient and condition: a newborn with spina bifida myelomeningocele.
  • Next, understand the question's focus: it asks for a sign of an associated complication, not a sign of the primary condition itself.
  • Recall or deduce the most common and serious complication of myelomeningocele. This is hydrocephalus, due to the high incidence of associated Chiari II malformation.
  • Evaluate each option to determine which one is a direct sign of hydrocephalus in a newborn.
  • Option A (Bulging fontanelle) is a classic sign of increased intracranial pressure in an infant.
  • Eliminate the other options by identifying why they are incorrect: Option B is a sign of a different condition (spina bifida occulta), Option C indicates the opposite problem (dehydration), and Option D describes the opposite neurological finding (myelomeningocele causes diminished, not hyperactive, reflexes).
Concept Tested & Keywords
  • Concept Tested: Assessment of Complications in Myelomeningocele
  • Stem keywords: newborn, spina bifida myelomeningocele, clinical sign, associated complication
  • Lead-in keywords: most strongly suggests
  • Clinical cues: Newborn with myelomeningocele: This patient population has a very high risk (up to 95%) of developing hydrocephalus, making assessment for this complication a top priority.

Question ID

Q7P6_0ykVZW-fUYyEqG31J

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